
Iowa Birth Defect Data
Iowa Birth Defects Counts and Prevalence, 2017-2021
(Prevalence per 10,000 live births)
Disorder | Total Counts | Total Prevalence | White, non-Hispanic | Prevalence | Black, non-Hispanic | Prevalence | Hispanic | Prevalence | Asian or Pacific Islander | Prevalence | Native American or Alaskan Native | Prevalence | Other/Unknown |
---|---|---|---|---|---|---|---|---|---|---|---|---|---|
Anencephalus | 55 | 2.9 | 5 | 0.3 | 0 | 0.0 | 1 | 0.5 | 3 | 4.1 | 0 | 0.0 | 46 |
Anophthalmia/microphthalmia | 30 | 1.6 | 19 | 1.3 | 3 | 2.3 | 4 | 2.2 | 0 | 0.0 | 1 | 13.2 | 3 |
Anotia/microtia | 54 | 2.9 | 37 | 2.6 | 0 | 0.0 | 11 | 5.9 | 4 | 5.5 | 1 | 13.2 | 1 |
Aortic valve stenosis | 45 | 2.4 | 38 | 2.6 | 1 | 0.8 | 4 | 2.2 | 0 | 0.0 | 0 | 0.0 | 2 |
Atrial septal defect | 387 | 20.7 | 266 | 18.5 | 38 | 28.6 | 45 | 24.3 | 18 | 24.8 | 3 | 39.7 | 17 |
Atrioventricular septal defect (endocardial cushion defect) | 105 | 5.6 | 77 | 5.4 | 6 | 4.5 | 12 | 6.5 | 4 | 5.5 | 2 | 26.5 | 4 |
Biliary atresia | 5 | 0.3 | 2 | 0.1 | 2 | 1.5 | 0 | 0.0 | 1 | 1.4 | 0 | 0.0 | 0 |
Bladder exstrophy | 6 | 0.3 | 4 | 0.3 | 0 | 0.0 | 2 | 1.1 | 0 | 0.0 | 0 | 0.0 | 0 |
Choanal atresia | 10 | 0.5 | 9 | 0.6 | 1 | 0.8 | 0 | 0.0 | 0 | 0.0 | 0 | 0.0 | 0 |
Cleft lip alone | 71 | 3.8 | 57 | 4.0 | 3 | 2.3 | 6 | 3.2 | 2 | 2.8 | 0 | 0.0 | 3 |
Cleft lip with cleft palate | 128 | 6.9 | 84 | 5.8 | 6 | 4.5 | 14 | 7.6 | 4 | 5.5 | 1 | 13.2 | 19 |
Cleft palate alone | 139 | 7.4 | 108 | 7.5 | 11 | 8.3 | 11 | 5.9 | 4 | 5.5 | 2 | 26.5 | 3 |
Clubfoot | 341 | 18.3 | 246 | 17.1 | 19 | 14.3 | 24 | 13.0 | 18 | 24.8 | 1 | 13.2 | 33 |
Coarctation of aorta | 128 | 6.9 | 100 | 7.0 | 8 | 6.0 | 13 | 7.0 | 4 | 5.5 | 2 | 26.5 | 1 |
Common truncus (truncus arteriosus) | 13 | 0.7 | 6 | 0.4 | 0 | 0.0 | 3 | 1.6 | 0 | 0.0 | 0 | 0.0 | 4 |
Congenital Cataract | 67 | 3.6 | 51 | 3.5 | 5 | 3.8 | 8 | 4.3 | 3 | 4.1 | 0 | 0.0 | 0 |
Congenital posterior urethral valves | 21 | 2.2 | 15 | 2.0 | 4 | 6.0 | 0 | 0.0 | 2 | 5.3 | 0 | 0.0 | 0 |
Craniosynostosis | 119 | 6.4 | 104 | 7.2 | 0 | 0.0 | 9 | 4.9 | 3 | 4.1 | 0 | 0.0 | 3 |
Deletion 22q11.2 | 30 | 1.6 | 26 | 1.8 | 1 | 0.8 | 2 | 1.1 | 0 | 0.0 | 0 | 0.0 | 1 |
Diaphragmatic hernia | 63 | 3.4 | 47 | 3.3 | 3 | 2.3 | 2 | 1.1 | 4 | 5.5 | 0 | 0.0 | 7 |
Double outlet right ventricle (DORV) | 48 | 2.6 | 27 | 1.9 | 5 | 3.8 | 4 | 2.2 | 2 | 2.8 | 0 | 0.0 | 10 |
Ebsteins’s anomaly | 16 | 0.9 | 12 | 0.8 | 3 | 2.3 | 1 | 0.5 | 0 | 0.0 | 0 | 0.0 | 0 |
Encephalocele | 22 | 1.2 | 6 | 0.4 | 1 | 0.8 | 1 | 0.5 | 2 | 2.8 | 0 | 0.0 | 12 |
Esophageal atresia/tracheoesophageal fistula | 49 | 2.6 | 34 | 2.4 | 7 | 5.3 | 5 | 2.7 | 1 | 1.4 | 0 | 0.0 | 2 |
Gastroschisis | 54 | 2.9 | 42 | 2.9 | 1 | 0.8 | 5 | 2.7 | 1 | 1.4 | 0 | 0.0 | 5 |
Hirschsprung’s disease (congenital megacolon) | 30 | 1.6 | 26 | 1.8 | 1 | 0.8 | 2 | 1.1 | 1 | 1.4 | 0 | 0.0 | 0 |
Holoprosencephaly | 47 | 2.5 | 15 | 1.0 | 1 | 0.8 | 3 | 1.6 | 3 | 4.1 | 0 | 0.0 | 25 |
Hypoplastic left heart syndrome | 48 | 2.6 | 29 | 2.0 | 7 | 5.3 | 5 | 2.7 | 1 | 1.4 | 0 | 0.0 | 6 |
Hypospadias | 571 | 59.9 | 495 | 67.3 | 34 | 50.8 | 30 | 31.9 | 8 | 21.4 | 1 | 27.2 | 3 |
Interrupted aortic arch (IAA) | 15 | 0.8 | 10 | 0.7 | 1 | 0.8 | 2 | 1.1 | 0 | 0.0 | 0 | 0.0 | 2 |
Limb deficiencies (reduction defects) | 102 | 5.5 | 60 | 4.2 | 5 | 3.8 | 8 | 4.3 | 5 | 6.9 | 0 | 0.0 | 24 |
Omphalocele | 52 | 2.8 | 21 | 1.5 | 4 | 3.0 | 2 | 1.1 | 1 | 1.4 | 0 | 0.0 | 24 |
Pulmonary valve atresia and stenosis | 173 | 9.3 | 135 | 9.4 | 16 | 12.0 | 11 | 5.9 | 9 | 12.4 | 0 | 0.0 | 2 |
Pyloric stenosis | 275 | 14.7 | 233 | 16.2 | 8 | 6.0 | 28 | 15.1 | 2 | 2.8 | 1 | 13.2 | 3 |
Rectal and large intestinal atresia/stenosis | 61 | 3.3 | 41 | 2.9 | 5 | 3.8 | 6 | 3.2 | 7 | 9.6 | 0 | 0.0 | 2 |
Renal agenesis/hypoplasia | 127 | 6.8 | 83 | 5.8 | 6 | 4.5 | 11 | 5.9 | 11 | 15.2 | 0 | 0.0 | 16 |
Single ventricle | 10 | 0.5 | 6 | 0.4 | 0 | 0.0 | 1 | 0.5 | 0 | 0.0 | 0 | 0.0 | 3 |
Small intestinal atresia/stenosis | 53 | 2.8 | 41 | 2.9 | 2 | 1.5 | 4 | 2.2 | 6 | 8.3 | 0 | 0.0 | 0 |
Spina bifida without anencephalus | 76 | 4.1 | 50 | 3.5 | 3 | 2.3 | 3 | 1.6 | 4 | 5.5 | 1 | 13.2 | 15 |
Tetralogy of Fallot | 77 | 4.1 | 56 | 3.9 | 10 | 7.5 | 3 | 1.6 | 2 | 2.8 | 0 | 0.0 | 6 |
Total anomalous pulmonary venous connection | 24 | 1.3 | 18 | 1.3 | 0 | 0.0 | 4 | 2.2 | 1 | 1.4 | 1 | 13.2 | 0 |
Transposition of great arteries (TGA) | 50 | 2.7 | 38 | 2.6 | 0 | 0.0 | 5 | 2.7 | 4 | 5.5 | 1 | 13.2 | 2 |
Tricuspid valve atresia and stenosis | 44 | 2.4 | 24 | 1.7 | 6 | 4.5 | 5 | 2.7 | 5 | 6.9 | 0 | 0.0 | 4 |
Trisomy 13 (Patau syndrome) | 30 | 1.6 | 11 | 0.8 | 1 | 0.8 | 0 | 0.0 | 0 | 0.0 | 0 | 0.0 | 18 |
Trisomy 18 (Edwards syndrome) | 66 | 3.5 | 16 | 1.1 | 3 | 2.3 | 3 | 1.6 | 7 | 9.6 | 1 | 13.2 | 36 |
Trisomy 21 (Down syndrome) | 302 | 16.2 | 193 | 13.4 | 23 | 17.3 | 37 | 20.0 | 9 | 12.4 | 3 | 39.7 | 37 |
Turner syndrome | 39 | 4.3 | 13 | 1.9 | 0 | 0.0 | 2 | 2.2 | 3 | 8.5 | 0 | 0.0 | 21 |
Ventricular septal defect | 943 | 50.5 | 704 | 49.0 | 72 | 54.1 | 93 | 50.3 | 31 | 42.7 | 5 | 66.2 | 38 |